Patho Patho #40

Question

The nurse is performing education for a client newly diagnosed with polycystic kidney disorder. Which information should the nurse include in teaching?

Answers

  1. “The classic signs of this disorder include flank pain and a single mass in the abdominal area.”
    • Rationale:

      This answer choice is not correct because the classic manifestations of PKD are not flank pain and a single mass. Flank pain is more characteristic of a urinary tract infection and a single mass more characteristic of a tumor.

  2. “This is a genetic disorder that has an autosomal dominant inheritance pattern.”
    • Rationale:

      This answer is correct because PKD is a genetic disorder with an autosomal dominant pattern of inheritance. This is important information to include in client teaching/ genetic counseling.

  3. “There is no chance that you could pass this disorder on to your children in the future.”
    • Rationale:

      This answer choice is not correct because PKD has an autosomal dominant pattern of inheritance meaning that only one copy of the mutated gene is necessary for the client’s children to display characteristics of the disorder.

  4. “Polycystic kidney disease should not cause any abdominal discomfort so this would need to be reported to your provider immediately.”
    • Rationale:

      This answer choice is not correct because some degree of abdominal discomfort is expected in clients with PKD.

Overview

Polycystic kidney disorder (PKD) is a genetic syndrome in which the renal tubules become structurally abnormal. This results in multiple cystic like growths within the kidneys. PKD is caused by the inheritance of abnormal genes that produce a protein that adversely affects renal tubule development. The pattern of inheritance of PKD is one of autosomal dominant inheritance.

Explanation

Learning Outcomes

This question is asking the nurse to choose information that is important to provide when educating a client newly diagnosed with polycystic kidney disorder. PKD is a genetic disorder with an autosomal dominant pattern of inheritance. This is important information to include in teaching especially for clients who plan to have children.

Test Taking Tip

With autosomal dominant disorders, one copy of a mutated gene passed from parent to child can result in the child developing the condition. With autosomal recessive inheritance, two copies of a mutated gene are necessary in order for a child to develop the condition.

Video Rationale