Medical Surgical Cystic fibrosis #1

Question

The nurse is providing home care education to the parents of a child recently diagnosed with cystic fibrosis. Which will the nurse include in her teaching plan? Select all that apply.

Answers

  1. Chest physiotherapy before and after meals.
    • Rationale:

      This answer is not correct because chest physiotherapy is indicated in the mornings and at night, not before and after meals due to the chance of emesis. Chest physiotherapy helps loosen and mobilize secretions.

  2. Instruction on vaccination importance.
    • Rationale:

      This answer is correct because the client with cystic fibrosis is at higher risk for complications from preventable illnesses. Studies have suggested adverse outcomes in terms of lung function and disease progression in clients following an infection of influenza or pneumonia. Pulmonary exacerbations are most frequently associated with clients diagnosed with CF.

  3. Provide information about the Cystic Fibrosis Foundation.
    • Rationale:

      This answer is correct because the Cystic Fibrosis Foundation is an advocacy group that is dedicated to improving the daily lives of those living with cystic fibrosis. They offer a plethora of information on new drug developments, clinical trials, and helping clients find specialised CF care near their home. This is a great support for the caretakers of those with CF.

  4. Monitor for hemoptysis and proper treatment.
    • Rationale:

      This answer is correct because hemoptysis can indicate a lung infection in the client with CF. Hemoptysis is coughing up blood and is controlled with bedrest, cough suppressants, antibiotics, and vitamin K. If hemoptysis is persistent, the site of bleeding may be cauterized.

  5. Use of a mucus clearance device.
    • Rationale:

      This answer is correct because this device helps remove mucus. It is a small hand-held device with a plastic pipe and a stainless steel ball inside. It works by the client exhaling into the device and the ball inside vibrates. This vibration travels back into the lungs and helps to loosen mucus. Gentle coughing then removes the mucus.

Overview

Cystic fibrosis (CF) is a hereditary disease where the body produces thick and sticky mucus that can clog the lungs and obstruct the pancreas. The child with CF will require many interventions performed by the parents in the home environment.

Explanation

Learning Outcomes

Cystic fibrosis (CF) is a hereditary disease where the body produces thick and sticky mucus that can clog the lungs and obstruct the pancreas. The child with CF will require many interventions performed by the parents in the home environment. Chest physiotherapy is performed in the mornings and at night, to help loosen and mobilize secretions. It can be performed more often when the client is ill with a respiratory illness. Due to the client with CF being at high risk for complications of illness, vaccines are recommended. The Cystic Fibrosis Foundation is an advocacy group that is dedicated to improving the daily lives of those living with cystic fibrosis and are a great support for the caretakers of those with CF. Monitoring for hemoptysis is recommended to help prevent infection. Copious amounts should be treated immediately. Mucus clearing devices are of great assistance to the client with CF, helping expel thick mucus.

Test Taking Tip

Nursing education is a large part of a nurse’s job. Be prepared to educate clients and caretakers on their specific illnesses or diseases.

Video Rationale